Table 9 Guidance statements for decompression of the spinal cord, spinal stabilisation and thoracolumbar kyphoscoliosis
From: Recommendations for the management of MPS VI: systematic evidence- and consensus-based guidance
Statement | Percentage consensus |
|---|---|
Decompression of the spinal cord is recommended in patients with MPS VI who have evidence of spinal cord compression based on clinical and radiographica findings Evidence Grade: D (limited published evidence) | 97% |
Spinal stabilisation of the craniocervical junction with either cervical fusion or occipital-cervical fusion is recommended in patients with MPS VI who have evidence of significant instability Evidence Grade: D (expert clinical opinion) | 100% |
Correction of thoracolumbar kyphoscoliosis is recommended in patients with MPS VI who present with progressive radiographic changes, intractable pain and clinical deterioration as defined by gait, lung function and changes in the degree of kyphosis Evidence Grade: D (limited published evidence) | 97% |