Table 12 Guidance statements for cardiac valve replacement, left ventricular apical aneurysms and tracheostomy
From: Recommendations for the management of MPS VI: systematic evidence- and consensus-based guidance
Statement | Percentage consensus |
|---|---|
Cardiac (aortic, mitral) valve replacement should be considered in patients with MPS VI who display symptomatic and severe valve stenosis or regurgitation Evidence Grade: C (level 4 studies) | 100% |
Left ventricular apical aneurysms occur rarely in patients with MPS VI, but should be resected whenever possible Evidence Grade: D (limited published evidence) | 85% |