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Table 12 Guidance statements for cardiac valve replacement, left ventricular apical aneurysms and tracheostomy

From: Recommendations for the management of MPS VI: systematic evidence- and consensus-based guidance

Statement Percentage consensus
Cardiac (aortic, mitral) valve replacement should be considered in patients with MPS VI who display symptomatic and severe valve stenosis or regurgitation
Evidence Grade: C (level 4 studies)
Left ventricular apical aneurysms occur rarely in patients with MPS VI, but should be resected whenever possible
Evidence Grade: D (limited published evidence)