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Table 1 Clinical areas of focus and recommended speciality focus

From: Recommendations for the management of MPS VI: systematic evidence- and consensus-based guidance

Table Recommended speciality focus
Table 2: General principles for the management of patients with MPS VI all
Table 3: Recommended routine monitoring and assessments in patients with MPS VI all
Table 4: Guidance statement for galsulfase geneticist, metabolic physician, paediatrician, nurse, physiotherapist
Table 5: Guidance statements for HSCT anaesthetist, bone marrow transplant expert/hematopoietic stem cell transplant expert, geneticist, paediatrician, nurse
Table 6: Guidance statements for continuous positive airway pressure (CPAP), non-invasive positive pressure ventilation (NIPPV), oxygen supplementation and hypercapnia monitoring anaesthetist, ear-nose-throat specialist, geneticist, paediatrician, respiratory physician/pulmonologist, nurse
Table 7: Guidance statements for anaesthesia all
Table 8: Guidance statements for hip reconstruction, hip replacement and growth modulation surgeries anaesthetist, geneticist, orthopaedic surgeon, neurosurgeon, paediatrician, physiotherapist
Table 9: Guidance statements for decompression of the spinal cord, spinal stabilisation and thoracolumbar kyphoscoliosis anaesthetist, geneticist, orthopaedic surgeon, neurosurgeon, paediatrician, physiotherapist
Table 10: Guidance statement for corneal transplantation anaesthetist, geneticist, ophthalmologist, paediatrician
Table 11. Guidance statements for decompression of the median nerve, tenosynovectomy and pulley release anaesthetist, geneticist, hand surgeon, orthopaedic surgeon, neurosurgeon, paediatrician
Table 12: Guidance statement for cardiac valve replacement and left ventricular apical aneurysms anaesthetist, cardiologist, geneticist, paediatrician
Table 13: Guidance statements for tonsillectomy and/or adenoidectomy, tracheostomy and insertion of ventilation tubes anaesthetist, geneticist, ear-nose-throat specialist, paediatrician, respiratory physician/pulmonologist