Variable | TSC N = 16 | Sporadic N = 44 | Control N = 25 | P |
---|---|---|---|---|
Age (years) (mean ± SE) | 41.6 ± 2.9 | 49.4 ± 1.8 | 39.4 ± 3.2 | 0.0031 |
FEV1 (%) (mean ± SE)5 | 90.9 ± 4.3 | 86.7 ± 3.6 | – | 0.462 |
FVC (%) (mean ± SE)5 | 99.6 ± 3.7 | 98.1 ± 3.0 | – | 0.752 |
DLCO (%) (mean ± SE)6 | 65.9 ± 5.9 | 67.7 ± 2.9 | – | 0.683 |
Endostatin (ng/mL) (mean ± SE) | 54.2 ± 6.1 | 28.9 ± 2.1 | 30.1 ± 4.0 | 0.00071 |
AML | ||||
No, n (%) | 0 (0) | 25 (56.8) | – | 0.000054 |
Yes, n (%) | 16 (100) | 19 (43.2) | ||
Isolated Reduction in DLCO (< 60%) 6 | ||||
No, n (%) | 11 (68.8) | 39 (95.1) | – | 0.0154 |
Yes, n (%) | 5 (31.2) | 2 (4.9) |