|
Factors considered “very important” in deciding which formula to prescribea
|
|
Nutrient composition of formula
|
18 (95)
|
|
Patient’s age
|
17 (89)
|
|
Preferences of the patient or family
|
17 (89)
|
|
Availability of the product
|
15 (79)
|
|
Price of the product
|
4 (21)
|
|
Severity of PAH deficiency
|
4 (21)
|
|
Approaches to assessing patient adherence to formula and diet prescriptiona
|
|
By patient’s/caregiver’s verbal report
|
17 (89)
|
|
Monitoring weight and height
|
15 (79)
|
|
By laboratory tests:
| |
|
Phenylalanine
|
16 (84)
|
|
Pre-albumin
|
13 (68)
|
|
Tyrosine
|
13 (68)
|
|
Iron
|
12 (63)
|
|
B12
|
12 (63)
|
|
Albumin
|
5 (26)
|
|
Checking how much formula was released by the dispensing authority
|
12 (63)
|
|
By analyzing written dietary questionnaires
|
10 (53)
|
|
Technique that is most successful in improving adherence to diet
|
|
Individualized PAH deficiency nutrition counseling
|
11 (58%)
|
|
Motivational interview techniques
|
4 (21%)
|
|
Reporting results of blood dots to patients
|
4 (21%)
|
|
Regular reminders for Phe blood dots
|
0
|
|
Nutrients that are routinely monitored for “most” patients, based on diet recordsa
|
|
Dietary Phe intake
|
19 (100%)
|
|
Protein intake
|
18 (95%)
|
|
Calorie intake
|
14 (74%)
|
|
Mineral intake (any)
|
12b (67%)
|
|
Vitamin intake (any)
|
12 (63%)
|
|
Fat intake
|
5c (29%)
|
|
Other
|
0
|
|
Components that are always/often included in routine clinical visit assessmentsa
|
|
Anthropometric measurements
|
19 (100)
|
|
Diet education
|
17 (90)
|
|
Dietary analysis
|
17 (90)
|
