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Table 1 Cohort characteristics

From: Gynecologic assessment of 19 adult females with cartilage-hair hypoplasia – high rate of HPV positivity

 

N

Age group (yrs)

 

 19–30

7

 31–40

3

 41–50

4

 51–60

0

 > 60

5

Height (cm)

 < 115

5

 115–130

10

 > 130

4

Reproductive health

Menarche (median, yrs)

12.5

Cycle length (variation, median, days)

21–60, 28

Menstrual flow

 sparse

2

 normal

15

 heavy

2

Pregnancies

6/19

Births

 0

14

 1–2

1

 > 2

4

Current hormonal therapy

5/19

 Combined contraception pills

1

 Progestin only -pills

2

 Hormone replacement therapy

2

Immunodeficiency

Suseptibility to infectionsa

 Yes

9

 Intermediate

4

 Normal

6

Previous skin warts

 Yes

4

 No

14

Repeated genital infections

6/19

Previous malignancyb

3

Leucocytes (× 109/L) (range, median)

3.2–13.4; 5.6

Lymphocytes (× 109/L) (range, median)

0.5–2.58; 1.22

Neutrophiles (× 109/L) (range, median)

1.74–10.65; 3.37

  1. aYes = one or several episodes of otitis media and/or rhinosinuitits; Intermediate = pneumonia necessitating hospitalization and/or recurrent otitis media and/or rhinosinuitis requiring surgical treatment
  2. b1 squamous cell carcinoma,2 basal cell carcinomas