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Table 1 Electroneurography examination results

From: Early detection of median nerve compression by Electroneurography can improve outcome in children with Mucopolysaccharidoses

Case Gender Diagnosis age at CTS surgery (months) age at ERT (months) Age at ENG (months) Distal Motor Latency MNL (msec) Distal Sensory Latency SNL (msec) Distal Motor Amplitude CMAP (mVlt) Distal Sensory Amplitude SEPA (μVlt)
right left right left right left right left
N°1 M Hunter 84 125 55 3.8 (+2.5 SD) 4.2 (+3 SD) 2.6 (+2 SD) 3.6 (+4 SD) 3.7 (77%) 3.0 (62%) 9.4 (47%) 8.7 (43%)
      70 4.7 (+3.5 SD) 5.8 (+6 SD) 3.2 (+3 SD) absent 0.6 (12%) 1.1 (23%) 9.5 (47%) absent
      79 4.5 (+3 SD) 6.6 (+7 SD) 2.7 (+2 SD) absent 8.8 (183%) 6.2 (125%) 5.0 (22%) absent
N°2 M Hunter 141 145 146 5.0 (+3 SD) 3.5 (0 SD) 3.0 (+2 SD) 2.5 (0 SD) NA NA NA 4.1 (0%)
      179 2.3 (-1 SD) 3.5 (+0.8 SD) absent absent 3.1 (76%) 3.2 (77% ) absent absent
N°3 M Hunter 136 141 142 6.7 (+6 SD) 6.0 (+5 SD) 3.7 (+4 SD) 3.2 (+4 SD) 4.5 (110%) 4.5 (110%) 4.7 (31%) 8.3 (56%)
      167 4.1 (+1.5 SD) 3.7 (+1 SD) 2.8 (+1.5 SD) 2.5 (+0.5 SD) 3.8 (93% ) 3.9 (95%) 11.0 (74%) 23.3 (156%)
N°4 M Hunter 78 35 31 normal normal normal normal normal normal normal normal
      57 3.0 (+1 SD) 4.8 (+5 SD) 3.2 (+3 SD) 3.4 (+3.5 SD) 3.8 (80%) 5.3 (110%) 13.3 (66%) 14.0 (70%)
N°5 M Hunter 78 109 69 13.2 (+18 SD) 10.0 (+13 SD) absent absent 0.6 (13%) 0.6 (15%) absent absent
      76 11.0 (+14 SD) 10.7 (+14 SD) absent absent 0.7 (14%) 0.2 (4%) absent absent
      102 5.3 (+3 SD) 3.7 (+1 SD) 4.2 (+7 SD) 3.8 (+6 SD) 2.5 (73%) 5.6 (164%) 4.9 (38%) 5.0 (38%)
N°6 M Hunter 120 129 134 3.0 (0 SD) 4.0 (+1.5 SD) 3.4 (+3 SD) 3.12 (+2.5 SD) 4.9 (120%) 4.8 (117%) 1.9 (12%) 19.6 (130%)
N°7 M Hunter   68 115 4.5 (+2 SD) 4.3 (+2 SD) 3.3 (+4 SD) 3.3 (+4 SD) 8.3 (265%) 2.5 (74%) 8.5 (65%) 5.0 (38%)
N°8 M Hunter    72 3.7 (+3 SD) 3.5 (+2.5 SD) absent absent 0.6 (15%) 4.4 (110%) absent absent
N°9 M Hunter    44 5.4 (+5 SD) 4.7 (+4 SD) 3.8 (+5 SD) 3.0 (+1 SD) 1.9 (48%) 0.5 (13%) 10.6 (53%) 8.4 (42%)
N°10 M Hunter 53   43 4.2 (+3 SD) 4.9 (+7 SD) 2.4 (+1 SD) 3.8 (+5 SD) 4.3 (107%) 2.5 (62%) 25.0 (120%) 17.1 (85%)
N°11 M Hurler    56 5.1 (+4.5 SD) 4.1 (+3 SD) 4.1 (+5 SD) 2.5 (+1.5 SD) 1.0 (20%) 2.9 (60%) 3.7 (18%) 12.8 (65%)
N°12 F Hurler   12 18 2.4 (0 SD) 2.2 (0 SD) 128.0 (-2 SD) 1.1 (-2 SD) 7.2 (185%) 4.8 (125%) 29.6 (116%) 42.6 (167%)
N°13 M Hurler-Sheie 74 93 51 2.5 (0 SD) ND absent ND 5.2 (108%) ND absent ND
      64 2.0 (+0.5 SD) 2.2 (0 SD) absent absent 2.3 (49%) 4.6 (95% ) absent absent
      176 4.5 (+ 2.5 SD) 3.6 (+1 SD) absent absent 2.1 (51%) 5.9 (144%) absent absent
  1. CTS carpal tunnel syndrome, ND not done, NA not available, ERT Enzyme Replacement Therapy, ENG electroneurography evaluation, SD standard deviation, % percent of lower limit of normal (LLN)