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Table 1 Main clinical features

From: Autosomal-dominant transthyretin (TTR)-related amyloidosis is not a frequent CMT2 neuropathy “in disguise”

Total patients

98

Male

51

Female

47

Mean age

55 yr

Mean onset

46,4 ± 12,9 yr

Median onset

45 yr

Mean disease duration

8,9 ± 10,2 yr

Median disease duration

4,5 yr

Prevalent motor neuropathy

13,20%

Sensory motor neuropathy

86,80%

Hypoacusia

4%

Tremor

1%

  1. yr years