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Table 1 Main clinical features

From: Autosomal-dominant transthyretin (TTR)-related amyloidosis is not a frequent CMT2 neuropathy “in disguise”

Total patients 98
Male 51
Female 47
Mean age 55 yr
Mean onset 46,4 ± 12,9 yr
Median onset 45 yr
Mean disease duration 8,9 ± 10,2 yr
Median disease duration 4,5 yr
Prevalent motor neuropathy 13,20%
Sensory motor neuropathy 86,80%
Hypoacusia 4%
Tremor 1%
  1. yr years