Table 2 Overview of tasks used to assess cognitive functioning in ET AwPKU across different cognitive domains

 Attentional capacity

California Verbal Learning Test (CVLT) – List A trial 1 [33]

Choice Reaction Time [11, 34]

Conjoined Search [11]

Detection with Distractors [11]

Digit Span Forward (WAIS-R) [33]

Feature Search [11]

n-back (0-back and 1-back trials) [36]

Stroop colour [11, 33]

Stroop word [33]

Telephone Search Test (TEA) [45]

Video tracking [55]

 Vigilance/focus

Continuous Performance Test (CPT) – omission errors [33]

Rapid Visual Processing [11, 34]

Sustained Attention Dots (ANT) [40]

Dot Pattern Exercise (SVAT) [37]

Telephone Search Test with Counting (TEA) [45]

Test d2 [52]

 Processing speed

CPT – response rate [33]

Motor Screening Test – latency [48]

Saccadic Latency [38]

Simple Detection [11]

Simple Reaction Time (CANTAB) [34]

Finger Motor Speed Exercise (SVAT) [37]

Stockings of Cambridge – initial thinking time [48]

Trail Making Test-A [1, 2, 33, 52]

Attention Diagnostic Method [56]

WAIS-III (Processing Speed Index) [35]

 Complex executive functions

Brixton Test [45]

Elithorn Perceptual Maze Test [49]

Object alternation learning [36]

Set Shifting Visual (ANT) [42]

Six Elements Test [45]

Spatial Working Memory – Strategy [48]

Stockings of Cambridge [48]

Tower of Hanoi [11]

Tower of London [49]

Trail Making Test (TMT) B-A [11, 33, 35]

WAIS-III (Perceptual Organisation Index) [35]

Wisconsin Card Sorting Test (WCST) [11, 33, 49, 56]

 Inhibitory control

CPT [33]

Flanker [36, 42]

Go-nogo [44]

Set Shifting Visual (ANT) [42]

Stop Signal Task [34]

Stroop (interference) [11, 33]

Sustained Attention Dots (ANT) [40]

 Working memory

Corsi Block Tapping Test [11]

CVLT – perseverative error [33]

Digit Span – backward [11, 33]

Feature Integration (ANT) [40]

Letter Pattern Exercise (SVAT) [37]

Memory Search 2 Dimensional (ANT) [40]

n-back (2-back trials) [36]

Non-word Repetition [11]

Self-Ordered Pointing test [45]

Spatial Span [34]

Spatial Working Memory [34, 48]

Visuo-Spatial Sequencing (ANT) [40]

WAIS-III (Working Memory Index) [35]

 Verbal fluency

Animal naming [11, 33]

Controlled Oral Word Association Test [33, 35]

Letter fluency [11, 45]

 Basic language skills: semantic processing

Boston Naming Test [33]

Picture naming [11]

Blocked cyclic naming [47]

Emotional Prosody Discrimination test [47]

Hayling Sentence Completion Test – Part A [47]

Narrative production: Recalling the Cinderella story [47]

Non-emotional Prosody Discrimination test [47]

Peabody Picture Vocabulary Test – Revised (PPVT-R) [33]

Word reading [11]

Word spelling [11]

 Complex language skills

Appreciation of Humour test [47]

Blocked cyclic naming – semantic Inference [47]

Comprehension of Inferred Meaning test [47]

Conflicting prosody – attend to prosody test [47]

Hayling Sentence Completion Test – Part B [45, 47]

Metaphor Picture test [47]

Naming: semantic inference [11]

Narrative production: Recalling the Cinderella story [47]

Non-word reading [11]

Non-word spelling [11]

Phoneme deletion [11]

Similarities (WAIS-R/WASI) [11, 33]

Spoonerisms [11]

Vocabulary (WAIS-R/WASI) [11, 33]

WAIS-III (Verbal Comprehension Index) [35]

Perceptual judgement task [36]

 Immediate recall: verbal / visual

CVLT – List A trial 5 and trials 1–5 [33]

Paired Associates Verbal Learning – trial 1–5 [11]

Paired Associates Visual Learning [11]

Rey Auditory Verbal Learning Test (RAVLT) – Trial A1-A5 [11]

ROCFT – Immediate recall [49]

WMS-III [35]

 Delayed recall: verbal / visual

CVLT – Sort delayed recall and Long delayed recall [33]

Paired Associates Verbal Learning – delayed [11]

RAVLT – Delayed recall [11, 45] and retention [11]

ROCFT – Delayed recall [33, 45]

WMS-III [35]

 Recognition: verbal / visual

CVLT – Recognition memory [33]

Delayed Matching to a Sample [11]

RAVLT – Recognition [45]

ROCFT – Recognition [45]

WMS-III [35]

Motor skills

Digit Symbol (Substitution) Task [11, 33]

Grooved Pegboard [11, 33]

MLS [55]

Motor Screening Test – errors [48]

Pursuit (ANT) [42]

Social-cognitive abilities

Face Recognition (ANT) [41]

Faux-Pas Recognition Test [41]

Identification of Facial Emotions (ANT) [41]

Reading the Mind in the Eyes Task [41]

Visual-spatial abilities

Block design (WAIS-R) [33]

Picture arrangement (WAIS-R) [33]

Picture completion (WAIS-R) [33]

ROCFT – with copy/initial copy [33, 45, 49, 56]