Table 5 Baseline and follow-up echocardiographic parameters of seven Taiwanese patients with MPS IVA who received ERT for 3-6 years
No. | Age at start of ERT (years) | ERT duration (years) | LVMI (z score) | IVSd (z score) | LVPWd (z score) | |||
|---|---|---|---|---|---|---|---|---|
Baseline | Follow-up | Baseline | Follow-up | Baseline | Follow-up | |||
1 | 1.4 | 6.0 | 0.44 | -1.22 | 1.8 | 0.5 | 1.1 | -0.5 |
2 | 2.8 | 3.0 | 0.46 | -1.24 | 2.0 | 1.0 | 0.2 | -2.2 |
6 | 7.3 | 4.0 | 2.47 | 2.64 | 1.2 | 2.2 | -0.1 | -0.2 |
11 | 13.9 | 3.0 | -1.46 | 0.05 | 5.2 | 3.1 | 0.9 | -0.5 |
20 | 14.9 | 4.1 | 1.09 | 1.47 | 4.3 | 1.9 | 0.4 | 0.0 |
23 | 16.8 | 4.1 | -1.41 | 0.25 | -0.1 | 0.5 | -1.9 | 0.1 |
31 | 25.8 | 4.4 | 3.8 | 3.17 | 2.4 | 6.0 | 2.3 | -0.2 |
Mean | 11.8 | 4.1 | 0.77 | 0.73 | 2.42 | 2.17 | 0.41 | -0.50 |
SD | 8.6 | 1.0 | 1.92 | 1.76 | 1.81 | 1.94 | 1.29 | 0.78 |