|
No.
|
Age at start of ERT (years)
|
ERT duration (years)
|
LVMI (z score)
|
IVSd (z score)
|
LVPWd (z score)
|
|---|
|
Baseline
|
Follow-up
|
Baseline
|
Follow-up
|
Baseline
|
Follow-up
|
|---|
|
1
|
1.4
|
6.0
|
0.44
|
-1.22
|
1.8
|
0.5
|
1.1
|
-0.5
|
|
2
|
2.8
|
3.0
|
0.46
|
-1.24
|
2.0
|
1.0
|
0.2
|
-2.2
|
|
6
|
7.3
|
4.0
|
2.47
|
2.64
|
1.2
|
2.2
|
-0.1
|
-0.2
|
|
11
|
13.9
|
3.0
|
-1.46
|
0.05
|
5.2
|
3.1
|
0.9
|
-0.5
|
|
20
|
14.9
|
4.1
|
1.09
|
1.47
|
4.3
|
1.9
|
0.4
|
0.0
|
|
23
|
16.8
|
4.1
|
-1.41
|
0.25
|
-0.1
|
0.5
|
-1.9
|
0.1
|
|
31
|
25.8
|
4.4
|
3.8
|
3.17
|
2.4
|
6.0
|
2.3
|
-0.2
|
|
Mean
|
11.8
|
4.1
|
0.77
|
0.73
|
2.42
|
2.17
|
0.41
|
-0.50
|
|
SD
|
8.6
|
1.0
|
1.92
|
1.76
|
1.81
|
1.94
|
1.29
|
0.78
|
- MPS mucopolysaccharidosis, ERT enzyme replacement therapy, LVMI left ventricular mass index, IVSd interventricular septum thickness in diastole, LVPWd left ventricular posterior wall thickness in diastole, SD standard deviation
