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Table 3 Ocular scoring in the Birmingham Epidermolysis Bullosa Severity Score

From: A review of scoring systems for ocular involvement in chronic cutaneous bullous diseases

Eyes

Score

No problem from EB

0

Occasional soreness

1

Frequent soreness

2

Persistent soreness

Early visible external eye disease

3

Between Score 3 and 5

4

Bilateral sight-threatening eye disease

5

  1. Adapted from: Moss C, Wong A, Davies P. The Birmingham Epidermolysis Bullosa Severity score: development and validation. Br J Dermatol. 2009;160:1057–1065