From: The complete European guidelines on phenylketonuria: diagnosis and treatment
Reference | Number of patients | 1st trimester | 2nd trimester | 3rd trimester |
---|---|---|---|---|
Vockley et al. 2014 [102] | 0 (USA guidelines) | 265–770 mg/day | 400–1650 mg/day | 700–2275 mg/day |
Acosta et al. 2001 [350] | 240 | 456 ± 233 to 684 ± 413 mg/day | 528 ± 269 to 528 ± 269 mg/day | 938 ± 542 to 1248 ± 513 mg/day |
Thompson et al. 1991 [351] | 1 | 6Â mg/kg bodyweight/day | Â | 30Â mg/kg bodyweight/day |
Kohlschutter et al. 2009 [343] | 3 | 400Â mg/day | Â | 1700Â mg/day (non-foetal PKU) maximum 600Â mg/day (foetal PKU) |
Duran et al. 1999 [232] | 5 | 250–500 mg/day | 300–500 mg/day |  |
Rohr et al. 1987 [369] | 3 | 450–800 mg/day | 720–1300 mg/day | 1300–1500 mg/day |