From: The complete European guidelines on phenylketonuria: diagnosis and treatment
Author | Tyr supplementation |
---|---|
Coutts 1979 [358] | >10Â g/day |
6000 to 7600Â mg/day | |
Rohr et al. 1987 [369] | Up to 6 g/d (did not ↑ blood Tyr >30 μmol/l) |
Davidson et al. 1989 [364] | 6.4–11.9 g/day |
Brenton et al. 1996 [363] | 2Â g/day |
Maillot et al. 2007 [333] | 8Â g/day (total from Phe-free L-amino acid supplements and Tyr supplements) |
Thompson et al. 1991 [351] | 160Â mg/kg/day- starting point and then titrate according to Tyr levels |