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Table 12 Reported Tyr supplementation during pregnancy in maternal PKU

From: The complete European guidelines on phenylketonuria: diagnosis and treatment

Author

Tyr supplementation

Coutts 1979 [358]

>10 g/day

Singh et al. 2014 [361], Vockley et al. 2014 [102]

6000 to 7600 mg/day

Rohr et al. 1987 [369]

Up to 6 g/d (did not ↑ blood Tyr >30 μmol/l)

Davidson et al. 1989 [364]

6.4–11.9 g/day

Brenton et al. 1996 [363]

2 g/day

Maillot et al. 2007 [333]

8 g/day (total from Phe-free L-amino acid supplements and Tyr supplements)

Thompson et al. 1991 [351]

160 mg/kg/day- starting point and then titrate according to Tyr levels