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Fig. 4 | Orphanet Journal of Rare Diseases

Fig. 4

From: Respiratory chain complex III deficiency due to mutated BCS1L: a novel phenotype with encephalomyopathy, partially phenocopied in a Bcs1l mutant mouse model

Fig. 4

Reduced Rieske iron-sulfur protein (RISP) immunoreactivity in patient brain. a Immunostaining for RISP in the occipital cortex of control and (b) patient brain. Cytoplasmic localization of RISP in cortical neuronal cells in control (c) and reduced amount of RISP immunoreactivity in the patient brain (d). Scale bars 100 μm

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