Table 2 Frequency of ARBDs from different provinces of Pakistan
ARBD | Sindh | Punjab | Federal capital | KPK | Total | Percentage | Previously reported cases from Pakistan¶ | Total | Local prevalence~ Per million | International prevalence* Per million |
|---|---|---|---|---|---|---|---|---|---|---|
VWD type 3 disorder | 05 | 62 | 21 | 7 | 95 | (33.8%) | 61 | 156 | 1.0 | 0.5 |
Fibrinogen deficiency | 11 | 20 | 3 | 0 | 34 | (12%) | 9 | 43 | 0.3 | 0.5 |
Glanzmann Thrombasthenia | 18 | 9 | 0 | 0 | 27 | (9.6%) | 50 | 77 | 0.5 | 1 |
Factor XIII deficiency | 7 | 2 | 4 | 0 | 13 | (4.6%) | 29 | 42 | 0.3 | 0.5 |
Factor VII deficiency | 4 | 6 | 1 | 1 | 12 | (4.3%) | 84 | 96 | 0.6 | 2 |
Factor V deficiency | 0 | 9 | 0 | 0 | 9 | (3.2%) | 28 | 37 | 0.2 | 1 |
Vitamin K dependent clotting factors deficiency | 0 | 7 | 0 | 1 | 8 | (2.8%) | 0 | 8 | 0.04 | 1 |
Bernard Soulier syndrome | 3 | 0 | 4 | 0 | 7 | (2.5%) | 5 | 12 | 0.07 | 1 |
Factor X deficiency | 1 | 1 | 0 | 0 | 2 | (0.7%) | 41 | 43 | 0.3 | 1 |
Factor II deficiency | 0 | 2 | 0 | 0 | 2 | (0.7%) | 10 | 12 | 0.07 | 0.5 |
Factor XI deficiency | 1 | 0 | 0 | 0 | 1 | (0.4%) | 1 | 2 | 0.01 | 1~ |
Combined Factor V & VIII deficiency | 1 | 0 | 0 | 0 | 1 | (0.4%) | 0 | 1 | 0.006 | 1 |