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Table 5 Arrhythmias in SMA type 3

From: Cardiac pathology in spinal muscular atrophy: a systematic review

Arrhythmias in patients with SMA type 3
Arrhythmia type Anatomical site of origin Reported ECG abnormalities
(number of times observed in patients with SMA type 3)
Impulse initiation disorder Sinus/SA node initiation disorders Sinus arrest (2)
Sinus dysfunction (1)
Sinus tachycardia (1)
Supraventricular initiation disorders Atrial fibrillation (5)
AV junctional rhythm (5)
Supraventricular extrasystoles (2)
Atrial flutter (2)
Atrial tachycardia (1)
Ventricular initiation disorders Ventricular extrasystoles (2)
Non-sustained ventricular tachycardias (2)
Impulse conduction disorders n/a Left anterior hemiblock (4)
AV-block (n.o.s.) (3)
Right bundle branch block (3)
1st degree AV block (3)
Complete AV block (2)
2nd degree AV block, Mobitz I (Wenckebach) (1)
Prolonged junctional recovery time (1)
  1. Reported arrhythmias in patients with SMA type 3 (n = 24). Some patients had more than one ECG abnormality. Also see Additional file 1: Table S3
  2. Abbreviations: SA sinoatrial; AV atrioventricular; n.o.s. not otherwise specified; n/a not applicable