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Table 12 PBZ and severity in clinical forms, percentage

From: Rett syndrome: a wide clinical and autonomic picture

PBZ areas Severity scale Classical Z-RTT Hanefeld ARTT-NOS
Motor
(0–36)
Mild 3.8 50
Medium 40.4 42.9 40
Severe 40.4 7.1 50 60
Extreme 15.4 50
S-C
(0–48)
Mild 17.3 50
Medium 40.4 35.7 50
Severe 34.6 14.3 50 30
Extreme 7.7 50 20
Daily living
(0–20)
Mild 7.7 42.9 20
Medium 30.8 42.9 16.7 60
Severe 44.02 14.3 33.3 10
Extreme 17.3 50 10
Total
(0–104)
Mild 9.6 71,4
Medium 82.7 28.6 66.7 100
Severe 7.7 33.3
Extreme