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Table 12 PBZ and severity in clinical forms, percentage

From: Rett syndrome: a wide clinical and autonomic picture

PBZ areas

Severity scale

Classical

Z-RTT

Hanefeld

ARTT-NOS

Motor

(0–36)

Mild

3.8

50

Medium

40.4

42.9

40

Severe

40.4

7.1

50

60

Extreme

15.4

50

S-C

(0–48)

Mild

17.3

50

Medium

40.4

35.7

50

Severe

34.6

14.3

50

30

Extreme

7.7

50

20

Daily living

(0–20)

Mild

7.7

42.9

20

Medium

30.8

42.9

16.7

60

Severe

44.02

14.3

33.3

10

Extreme

17.3

50

10

Total

(0–104)

Mild

9.6

71,4

Medium

82.7

28.6

66.7

100

Severe

7.7

33.3

Extreme