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Table 10 ISS areas and clinical forms

From: Rett syndrome: a wide clinical and autonomic picture

ISS areas Classical Z-RTT Hanefeld Congenital ARTT-NOS
Development
(n = 144)
Mean (SD) 4.2 (2.6) 1.4 (1.4) 4.4 (2.6) 9 (−) 5.5 (2.8)
Range 0–8 0–5 2–8 0–9
M_SKEL
(n = 146)
Mean (SD) 2.6 (1.8) 1.2 (1.1) 1.5 (0.9) 2 (−) 2.4 (1.7)
Range 0–6 0–5 0–3 0–5
Movement
(n = 147)
Mean (SD) 4.6 (1.4) 3.4 (1.3) 4.5 (1.1) 6 (−) 4.5 (1.5)
Range 0–8 1–6 3–6 2–8
Cortical
(n = 146)
Mean (SD) 3.8 (1.1) 2.5 (0.8) 5.1 (1) 4 (−) 3.9 (0.9)
Range 1–6 1–5 3–6 3–6
Brain
(n = 146)
Mean (SD) 4.3 (2) 3.3 (1.8) 4.5 (1.8) 5 (−) 5.1 (2.4)
Range 1–9 0–7 2–8 1–10