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Table 10 ISS areas and clinical forms

From: Rett syndrome: a wide clinical and autonomic picture

ISS areas

Classical

Z-RTT

Hanefeld

Congenital

ARTT-NOS

Development

(n = 144)

Mean (SD)

4.2 (2.6)

1.4 (1.4)

4.4 (2.6)

9 (−)

5.5 (2.8)

Range

0–8

0–5

2–8

0–9

M_SKEL

(n = 146)

Mean (SD)

2.6 (1.8)

1.2 (1.1)

1.5 (0.9)

2 (−)

2.4 (1.7)

Range

0–6

0–5

0–3

0–5

Movement

(n = 147)

Mean (SD)

4.6 (1.4)

3.4 (1.3)

4.5 (1.1)

6 (−)

4.5 (1.5)

Range

0–8

1–6

3–6

2–8

Cortical

(n = 146)

Mean (SD)

3.8 (1.1)

2.5 (0.8)

5.1 (1)

4 (−)

3.9 (0.9)

Range

1–6

1–5

3–6

3–6

Brain

(n = 146)

Mean (SD)

4.3 (2)

3.3 (1.8)

4.5 (1.8)

5 (−)

5.1 (2.4)

Range

1–9

0–7

2–8

1–10