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Table 4 Medication given during the initial crisis

From: Clinical course of 63 patients with neonatal onset urea cycle disorders in the years 2001–2013

 

CPS1D

OTCD

ASSD

All patients

Number of patients

12

23

27

63

Medication during initial crisis

 unclear

5 (21.7 %)

7 (25.9 %)

12 (19.0 %)

 yes

12 (100 %)

18 (78.3 %)

20 (74.1 %)

51 (81.0 %)

L-arginine

8 (66.7 %)

15 (65.2 %)

20 (74.1 %)

43 (68.3 %)

Benzoic acid

1 (8.3 %)

1 (1.6 %)

Carglumic acid

1 (8.3 %)

3 (13.0 %)

2 (7.4 %)

6 (9.5 %)

L-citrulline

1 (8.3 %)

2 (8.7 %)

3 (4.8 %)

Levocarnitine

3 (25.0 %)

7 (30.4 %)

8 (29.6 %)

18 (28.6 %)

Sodium benzoate

7 (58.3 %)

15 (65.2 %)

18 (66.7 %)

41 (65.1 %)

Sodium phenylacetate & sodium benzoate

2 (8.7 %)

2 (7.4 %)

4 (6.3 %)

Sodium phenylbutyrate

1 (8.3 %)

4 (17.4 %)

7 (25.9 %)

12 (19.0 %)

  1. Unclear means patients have not received medication or data were not entered