Fig. 1

Mass-specific mitochondrial (a) and mitochondrial-specific (b) respiratory capacity (normalised to Mito_VD). Respiratory capacities are presented for patients with mitochondrial myopathy in white bars and healthy controls in black bars) L_N, leak respiration without adenylates; P_ETF, fatty acid oxidative capacity; P_CI, respiratory capacity of complex I; P, oxidative phosphorylation capacity; L_Omy, oligomycin-induced leak respiration; E, electron transport system capacity; P_CII, respiratory capacity of complex II; ROX, residual oxygen consumption; COX, respiratory capacity of complex IV. Values are mean ± SD. *P < 0.05; **P < 0.01. n_Patients = 6, n_Controls = 8