From: Analysis of voice quality in patients with late-onset Pompe disease
ID | Czermak score | Oral cavity | Nose | Ears |
---|---|---|---|---|
1 | ND | N | DSN | N |
2 | ND | N | N | N |
3 | 2 | SP atonic, LMPh | N | N |
4 | ND | SP atonic, LMPh | N | N |
5 | 2 | Tonsillar hypertrophy, Short SP, Short SP | OMS bil | |
6 | 2 | SP atonic, short LMPh | N | N |
7 | 2 | Short atonic SP LMPh, atonic tongue | Conchal O | N |
8 | 2 | Short atonic SP, LMPh, atonic tongue | DSN | N |
9 | 0 | N | DSN | Epitympanal retr. |
10 | 1 | Short atonic SP, LMPh Lack of pharyngeal reflexes, Geographic tongue, Malocclusion (open bite) | N | N |
11 | 0 | N - Normal palate | N | N |
12 | 0 | SP LMPh | N | N |
13 | ND | ND | ND | ND |
14 | 0 | Long slender, movable, SP | DSN | N |
15 | 1 | N - Normal palate | N | Min. retractions of the drums |
16 | 0 | N - Normal palate | N | N |
17 | 0 | N - Normal palate Hypertrofia Tonsillae, | N | Osteoma in the right external auditory meatus |
18 | 1 | Short SP, PPHI, LMPh | DSN | N |
19 | 1 | Short SP, PPHI | Conchal O | Epitympanal retr. |