| | | | |
CAG repeat length (range)
|
---|
Group
|
n
|
Age at onset (range)
|
Age at baseline (range)
|
Follow-up period
|
Normal allele
|
Expanded allele
|
---|
SCA1
|
2
|
30.5y (30–31)
|
36y (36)
|
6.5y
|
30.5 (29–32)
|
50.5 (50–51)
|
SCA2
|
2
|
40.5y (37–44)
|
52.5y (50–55)
|
7y
|
21.5 (21–22)
|
41 (41)
|
SCA3
|
2
|
32.5y (25–40)
|
45y (37–50)
|
8y
|
16 (14–20)
|
72.3 (70–74)
|
SCA6
|
4
|
47.5y (28–59)
|
42.5y (41–65)
|
7y
|
12.3 (11–13)
|
22.5 (22–23)
|
SCA7
|
3
|
33.7y (29–38)
|
42.3y (38–50)
|
7y
|
13.7 (12–15)
|
56.3 (46–65)
|
- All values represent the group average (mean). Range values are given in brackets