Table 2 Measurements of urinary GAGs under weekly and biweekly dose regimens
Fold increase (mg/GAG/mmol creatinine) above reference range; N = within normal limits | ||||
|---|---|---|---|---|
Patient | Phenotype | T1 | T2 | T3 |
1 | H | 5 | N | N |
2 | H | 9 | N | N |
3 | H | 19 | 2.3 | 3.8 |
5 | HS | 16 | N | N |
6 | HS | 43 | N | N |
7 | HS | NA | 2.9 | N |
8 | HS | 4.4 | N | N |
9 | HS | 9 | N | N |
10 | HS | 23 | N | N |
11 | HS | 9.6 | N | N |
12 | HS | 4.8 | 1.2 | N |
14 | S | 5 | 1.2 | 2.9 |
16 | S | 7.9 | 2.4 | 1.8 |
17 | S | 148 | 1.1 | N |
18 | S | 3.7 | N | N |
19 | S | 1.7 | 2.1 | 1.2 |
20 | S | 2.7 | N | 1.2 |