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Fig. 1 | Orphanet Journal of Rare Diseases

Fig. 1

From: Severe tracheal and bronchial collapse in adults with type II mucopolysaccharidosis

Fig. 1

In- and expiratory chest CT scan. a Central airways measurements were performed at five locations: (a) 1 cm above aortic arch, (b) aortic arch, (c) 2 cm above carina bifurcation, (d) right main bronchus, (e) left main bronchus. b Tracheal cross section at “b” (1 cm above the aortic arch) in patient 2. Note abnormal “bell-shaped” trachea in the end-inspiration image. c At end expiration there is almost complete collapse of the trachea (same patient). d Bronchial cross section at “e”(left main bronchus) at end inspiration (patient 2) and e at end expiration (same patient). f Presence of trapped air at expiration (patient 1)

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