Fig. 9

Flow chart of risk stratification and indications to ICD in AC. The estimated risk of major arrhythmic events in the high-risk category is >10 %/year, in the intermediate-risk category ranges from 1 to 10 %/year, and in the low-risk category is <1 %/year. The high risk category includes patients who experienced cardiac arrest due to VF or sustained VT and most benefit from ICD (estimated annual event rate >10 %/year). The low risk category comprises probands and relatives without risk factors as well as healthy gene carriers (estimated annual event rate <1 %/year), who do not require any treatment. The intermediate risk category includes AC patients with ≥1 risk factors, except those mentioned in the high risk category (estimated annual event rate between 1 and 10 %/year). The decision to implant an ICD in these patients should be made on individual basis (from Ref.87, with permission). Abbreviations. SCD: sudden cardiac death; VF: ventricular fibrillation; VT: ventricular tachycardia; RV: right ventricle; LV: left ventricle