Fig. 1From: Carglumic acid enhances rapid ammonia detoxification in classical organic acidurias with a favourable risk-benefit profile: a retrospective observational studyPathophysiology of hyperammonaemia in organic acidurias and action of carglumic acid. CoA, coenzyme A; CPS-I, carbamoyl-phosphate synthase I; NAG, N-acetylglutamate; NAGS, N-acetylglutamate synthase; -, inhibition; +, activationBack to article page