Skip to main content

Table 2 Prevalence of rare lung diseases in New Zealand between 2009 and 2014– general population

From: Assessing the feasibility of a web-based registry for multiple orphan lung diseases: the Australasian Registry Network for Orphan Lung Disease (ARNOLD) experience

Disease

No. of reports

Per million

Acute idiopathic eosinophilic pneumonia

0

0.00

Children’s interstitial lung disease (ChILD)

0

0.00

Chronic idiopathic eosinophilic pneumonia

0

0.00

Churg-Strauss vasculitis

1

0.22

Congenital Malformations - Trachea

0

0.00

Cryptogenic organising pneumonia

2

0.44

Cystic lung lesions

1

0.22

Diaphragmatic Hernia

0

0.00

Diffuse panbronchiolitis

2

0.44

Drug reactions with eosinophilia

0

0.00

Extrinsic allergic alveolitis

3

0.66

Follicular bronchiolitis

0

0.00

Goodpasture syndrome

0

0.00

Hereditory haemorrhagic ataxia telangiectasia

0

0.00

Idiopathic pulmonary hemosiderosis

1

0.22

Langerhans cell histiocytosis

0

0.00

Lobar emphysema

0

0.00

Lymphangioleiomyomatosis

0

0.00

Obliterative bronchiolitis (not transplant related)

0

0.00

Other vasculitides incl. microscopic polyangiitis

1

0.22

Primary ciliary dyskinesia

3

0.66

Pulmonary alveolar proteinosis

0

0.00

Pulmonary amyloidosis

0

0.00

Tracheo-oesophageal fistula

0

0.00

Granulomatosis with polyangiitis

0

0.00

Total

14

3.10