Table 1 The seven principal ways a person can meet the Ghent II criteria in the Marfan syndrome diagnosis

1) Ascending aorta dilatation^a & ectopia lentis

2) Ascending aorta dilatation^a & a FBN1 mutation

3) Ascending aorta dilatation^a & minimum seven systematic points

4) Ectopia lentis with a FBN1 mutation known to cause ascending aorta dilatation^a

5) Family history of MFS & ectopia lentis

6) Family history of MFS & minimum seven systematic points

7) Family history of MFS & ascending aorta dilatation^a