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Table 1 Relationship between self-reported Sillence type and self-reported disease severity in adults with OI

From: Initial report of the osteogenesis imperfecta adult natural history initiative

   Self-reported disease severity
n (% of OI type)
OI type n (%) Mild Moderate Severe
I 369 (39) 308 (83) 59 (16) 2 (<1)
II 26 (3) 12 (46) 8 (31) 6 (23)
III 125 (13) 7 (1) 67 (20) 51(57)
IV 110 (12) 45 (41) 55 (50) 10 (9)
V 14 (1) 2 (14) 11 (79) 1 (7)
VI 2 (<1) 1 (50) 1 (50)
Bruck’s syndrome 3 (<1) 3 (100)
Unknown 295 (31) 154 (52) 123 (42) 18 (6)
Total 944 (100) 528 (56) 327 (35) 89 (9)
  1. Missing n = 15