Table 1 Relationship between self-reported Sillence type and self-reported disease severity in adults with OI
From: Initial report of the osteogenesis imperfecta adult natural history initiative
Self-reported disease severity | ||||
|---|---|---|---|---|
n (% of OI type) | ||||
OI type | n (%) | Mild | Moderate | Severe |
I | 369 (39) | 308 (83) | 59 (16) | 2 (<1) |
II | 26 (3) | 12 (46) | 8 (31) | 6 (23) |
III | 125 (13) | 7 (1) | 67 (20) | 51(57) |
IV | 110 (12) | 45 (41) | 55 (50) | 10 (9) |
V | 14 (1) | 2 (14) | 11 (79) | 1 (7) |
VI | 2 (<1) | – | 1 (50) | 1 (50) |
Bruck’s syndrome | 3 (<1) | – | 3 (100) | – |
Unknown | 295 (31) | 154 (52) | 123 (42) | 18 (6) |
Total | 944 (100) | 528 (56) | 327 (35) | 89 (9) |