Table 1 Outcome of paediatric chordomas observed in the major paediatric series of the literature.
From: Paediatric Chordomas
Author | Number of cases | Treatment | Mean follow-up in months (min-max) | Progression free survival (%) | Overall survival (%) | ||
|---|---|---|---|---|---|---|---|
Surgery | Radiotherapy | Chemotherapy | |||||
Benk et al.[ 19 ] | 18 | Partial resection (18) | Proton (18) | - | 72 (19–120) | 63 (5 years) | 68 (5 years) |
Borba et al.[ 16 ] | 79 (review) | Not precise | Not precise | Not precise | 39 (1–300) | - | 56.8 |
Hoch et al.[ 20 ] | 73 | Total/Partial resection (73) | Proton (73) | - | 90 (12–252) | - | 81 |
Ridenour et al.[ 18 ] | 20 | Partial (14) | Conventional (10) | (2) | 129 (1–501) | - | 63 |
Proton (2) | |||||||
None (2) | |||||||
Total (4) | Conventional (2) | ||||||
None (2) | |||||||
Biopsy (2) | Conventional (2) | ||||||
Necker - Lariboisière (not published) | 34 | Partial (24) | Conventional (2) | (3) | 78 (0.3-239) | 54.3 (15 years) | 63 |
Proton (3) | |||||||
Conventional + Proton (12) | |||||||
Radiosurgery (1) | |||||||
Tomotherapy (1) | |||||||
None (4) | |||||||
Unknown (1) | |||||||
Total (6) | Conventional (2) Proton (3) Conventional + Proton (1) | (1) | |||||
Unknown (4) | |||||||