Baseline parameter | Females | Males | Overall |
---|---|---|---|
N (%) | 24 (53.3) | 21 (46.7) | 45 |
Age, mean (SD), years | 38.6 (14.2) | 30.2 (9.5) | 34.7 (12.8) |
Age at ERT start, mean (SD), years | 38.7 (14.1) | 30.2 (9.5) | 34.7 (12.8) |
Age at ERT start, median (range), years | 37.2 (15.6–61.4) | 31.4 (14.9–44.9) | 34.5 (14.9–61.4) |
BMI, mean (SD), kg/m2 | 23.5 (3.6) | 21.6 (3.5) | 22.6 (3.6) |
Systolic BP, mean (SD), mmHg | 127.3 (13.2) | 126.2 (16.0) | 126.8 (14.4) |
Diastolic BP, mean (SD), mmHg | 72.3 (9.1) | 68.2 (10.3) | 70.4 (9.8) |
Heart rate, mean (SD), bpm | 64.0 (13.1) | 65.1 (7.7) | 64.5 (10.8) |
Diabetes, n (%) | 0 (0) | 0 (0) | 0 (0) |
Current smoker, n (%) | 2 (8.3) | 3 (14.3) | 5 (11.1) |
Arterial hypertension, n (%) | 2 (8.3) | 3 (14.3) | 5 (11.1) |