Skip to main content

Table 3 Cornell-Brown Scale (CBS) quality-of-life scores following HSCT for MLD

From: Long-term outcomes after allogeneic hematopoietic stem cell transplantation for metachromatic leukodystrophy: the largest single-institution cohort report

ID

MLD Subtype

Age (y,m)a

Post-HSCT follow-up (y,m)

Mood-related signs

Ideational disturbances

Behavioral disturbances

Physical signs

Cyclic functions

Total

3

LI

19,11

8,2

6

0

1

-1

-2

4

4

J

34,11

28,2

8

0

4

0

5

17

9

J

17,4

10,5

7

0

-1

-3

2

5

10

J

24,1

12,10

7

3

-1

0

0

9

16

J

22,11

12,3

5

6

-2

-1

1

9

17

J

19,4

5,3

5

0

-2

0

3

6

19

J

19,0

10,5

-5

1

-5

-2

-2

-13

22

J

21,7

9,0

3

3

3

2

-2

9

27

J

26,7

9,0

7

2

1

0

3

13

32

J

45,6

14,10

8

0

5

4

6

23

43

J

21,2

1,6

4

5

6

-1

0

14

39

A

49,9

5,7

0

2

0

0

3

5

  1. Total and sub-domain scores for evaluable long-term survivors using the CBS. More negative (less than zero) scores indicate decreasing quality-of-life; more positive (greater than zero) scores indicate increasing quality-of-life. LI Late-Infantile, J Juvenile, A Adult, a Age when survey administered, y Year, m Month