Skip to main content

Table 2 Associated conditions in 4 recently reported series of European patients with idiopathic non-cirrhotic portal hypertension

From: Idiopathic non-cirrhotic portal hypertension: a review

Reference Hillaire et al. [6] Cazals-Hatem et al. [11] Schouten et al. [10] Siramolpiwat et al. [2]
Prothrombotic disorder 6 PS deficiency 3 PS deficiency 3 PS deficiency 1 PS deficiency
2 PC deficiency 3 PC deficiency 3 PC deficiency 2 FII Leiden
2 MTHFR mutation 1 MTHFR mutation 1 FV Leiden
3 FII Leiden 2 FV Leiden
Haematological malignancy 1 0 4 5
Myeloproliferative neoplasm 6 10 3 0
Chronic HIV infection 0 0 5 15
Autoimmune disorder 3 10 1 9
Crohn’s disease 0 0 3 0
Genetic disorder 0 0 4 0
Solid organ malignancy 0 0 1 0
Azathioprine treatment 0 0 8 0
Arsenicals - 0 4 0
No associated conditions 12 31 26 30
Incomplete evaluation 2 - - 9
Totala 28 59 62 69
  1. FII factor II, FV Leiden factor V Leiden, HIV human immunodeficiency virus, MTHFR metilentetrahydorfolate reductase, PC protein C, PS protein S
  2. (a): Some patients have more than one associated condition