From: The hyperornithinemia–hyperammonemia-homocitrullinuria syndrome
Metabolites | HHH patients | Reference value |
---|---|---|
Ammonia | 215 ± 279 (18–2300) n = 93 | <55 |
Ornithine | 575 ± 265 (216–1915) n = 96 | 30-110 |
Citrulline | 26 ± 14 (1–57) n = 21 | 10-52 |
Glutamine | 1149 ± 592 (447–3688) n = 43 | 333-809 |
Arginine | 66 ± 26 (27–126) n = 22 | 20-112 |
Lysine | 178 ± 177 (35–858) n = 26 | 80-257 |