Figure 3
From: The hyperornithinemia–hyperammonemia-homocitrullinuria syndrome
The urea cycle and related patwhays. The acronyms correspond to: NAGS, N-acetylglutamate synthase; CPS, carbamyl-phosphate synthetase; OTC omithine transcarbamylase; ORC1, ornithine carrier 1; ASS argininosuccinate synthetase; ASL argininosuccinate lyase; NOS, nitric oxide synthase: ODC ortnithine decarboxylase; AGAT, argine: glycine amidinotransferase; GAMT, guanidinoacetate N-methyltransferase; OAT, ornithine delta-aminotransferase; P5CD 1- pyrrolin-e5-carboxylate dehydrogenase; P5CS, 1-pyrroline-5 carboxylate synthetase; P5CR,1-pyrroline-5-carboxylate reductase; PO, proline oxidase. The dashed circle indicates the multiprotien complex, which also includes cationic aminoacid transporter 1 (CAT1) and heat shock protein 90 (HSP 90).