Table 1 Demographic characteristics and laboratory assessments of Italian C1-INH-HAE patients
From: A nationwide survey of hereditary angioedema due to C1 inhibitor deficiency in Italy
Type I | Type II | Total | |
|---|---|---|---|
Patients (%) | 859 (87%) | 124 (13%) | 983 |
Gender (M/F) | 407/452 | 55/69 | 462/521 |
Median age (years) | 44 | 45 | 45 |
Median age at diagnosis (years) | 25 | 31 | 26 |
Antigenic C1-INH, median value (%) | 21 (IR 13-25) | 96 (IR 64-150) | 24 (IR 14-31) |
Funcitional C1-INH, median value (%) | 20 (IR 10-30) | 19 (IR 10-30) | 20 (IR 10-30) |
Antigenic C4, median value (%) | 20 (IR 10-25) | 21(IR 12-30) | 20 (IR 11-26) |