Clinical features and hemodynamic parameters | Carriers of c.1166A > C mutation | |
---|---|---|
Clinical data | p-value | |
Number | 38 | Â |
Gender | F/7Â M | 0.511 |
Age at diagnosis (years) | 49 ± 16 | 0.265 |
mPaP (mmHg) | 46 ± 13 | 0.035 |
sPaP (mmHg) | 69 ± 18 | 0.207 |
PVR (mmHg.l −1 .m −1 ) | 7.9 ± 2.8 | 0.035 |
CI (l.m −1 .m −2 ) | 2.4 ± 0.7 | 0.034 |
6MWT (m) | 413 ± 145 | 0.138 |