From: Treatment of motor and behavioural symptoms in three Lesch-Nyhan patients with intrathecal baclofen
Patient | Before ITB | After ITB |
---|---|---|
1 | Duration factor: 3 | Duration factor: 0 |
Motor severity factor: eyes and upper face: 1, lower face: 3, jaw and tongue: 2, larynx: 0, neck: 2, shoulder and proximal arm. 2, distal arm and hand (including elbow): 3, pelvis and proximal leg: 3, distal leg and foot (including knee): 2, trunk: 1. | Motor severity factor: eyes and upper face: 2, lower face: 1, jaw and tongue: 1, larynx: 0, neck: 1, shoulder and proximal arm 0, distal arm and hand (including elbow): 0, pelvis and proximal leg: 0, distal leg and foot (including knee): 0, trunk: 0. | |
Total = 22 | Total = 5 | |
2 | Duration factor: 4 | Duration factor: 0.5 |
Motor severity factor: eyes and upper face: 1, lower face: 4, jaw and tongue: 3, larynx: 0, neck: 4, shoulder and proximal arm. 4, distal arm and hand (including elbow): 4, pelvis and proximal leg: 4, distal leg and foot (including knee): 4, trunk: 1. | Motor severity factor: eyes and upper face: 1, lower face: 0, jaw and tongue: 1, larynx: 1, neck: 1, shoulder and proximal arm. 0, distal arm and hand (including elbow): 0, pelvis and proximal leg: 1, distal leg and foot (including knee): 0, trunk: 0. | |
Total = 23 | Total = 6.5 | |
3 | Duration factor: 4 | Duration factor: 1 |
Motor severity factor: eyes and upper face: 1, lower face: 4, jaw and tongue: 4, larynx: 0, neck: 3, shoulder and proximal arm. 3, distal arm and hand (including elbow): 2, pelvis and proximal leg: 3, distal leg and foot (including knee): 4, trunk: 0. | Motor severity factor: eyes and upper face: 1, lower face: 1, jaw and tongue: 2, larynx: 0, neck: 1, shoulder and proximal arm: 1, distal arm and hand (including elbow): 1, pelvis and proximal leg: 2, distal leg and foot (including knee): 1, trunk: 0. | |
Total = 38 | Total = 11 |