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Table 3 Detailed scores from patients’ UDRS scales

From: Treatment of motor and behavioural symptoms in three Lesch-Nyhan patients with intrathecal baclofen

Patient

Before ITB

After ITB

1

Duration factor: 3

Duration factor: 0

Motor severity factor: eyes and upper face: 1, lower face: 3, jaw and tongue: 2, larynx: 0, neck: 2, shoulder and proximal arm. 2, distal arm and hand (including elbow): 3, pelvis and proximal leg: 3, distal leg and foot (including knee): 2, trunk: 1.

Motor severity factor: eyes and upper face: 2, lower face: 1, jaw and tongue: 1, larynx: 0, neck: 1, shoulder and proximal arm 0, distal arm and hand (including elbow): 0, pelvis and proximal leg: 0, distal leg and foot (including knee): 0, trunk: 0.

Total = 22

Total = 5

2

Duration factor: 4

Duration factor: 0.5

Motor severity factor: eyes and upper face: 1, lower face: 4, jaw and tongue: 3, larynx: 0, neck: 4, shoulder and proximal arm. 4, distal arm and hand (including elbow): 4, pelvis and proximal leg: 4, distal leg and foot (including knee): 4, trunk: 1.

Motor severity factor: eyes and upper face: 1, lower face: 0, jaw and tongue: 1, larynx: 1, neck: 1, shoulder and proximal arm. 0, distal arm and hand (including elbow): 0, pelvis and proximal leg: 1, distal leg and foot (including knee): 0, trunk: 0.

Total = 23

Total = 6.5

3

Duration factor: 4

Duration factor: 1

Motor severity factor: eyes and upper face: 1, lower face: 4, jaw and tongue: 4, larynx: 0, neck: 3, shoulder and proximal arm. 3, distal arm and hand (including elbow): 2, pelvis and proximal leg: 3, distal leg and foot (including knee): 4, trunk: 0.

Motor severity factor: eyes and upper face: 1, lower face: 1, jaw and tongue: 2, larynx: 0, neck: 1, shoulder and proximal arm: 1, distal arm and hand (including elbow): 1, pelvis and proximal leg: 2, distal leg and foot (including knee): 1, trunk: 0.

Total = 38

Total = 11