Table 1 Laboratory parameters and echocardiographic studies in patient 1
From: Glycogen storage disease type III: modified Atkins diet improves myopathy
Time | |||||||||
|---|---|---|---|---|---|---|---|---|---|
Parameter | −6 m | −3 m | 0 m | +4 m | +8 m | +12 m | +18 m | +24 m | +32 m |
Metabolic monitoring | |||||||||
KB [mM] | - | - | - | 5.6 | 7.8 | 5.9 | 4.5 | 3.0 | 2.7 |
CK [U/l] (<170) | 2646 | 3400 | 2650 | 1735 | 670 | 602 | 621 | 668 | 599 |
Lipids | |||||||||
LDL-C [mg/dl] (<130) | 126 | 120 | 111 | 120 | 115 | 125 | 140 | 118 | 130 |
TG [mg/dl] (<140) | 180 | 184 | 180 | 183 | 192 | 180 | 224 | 181 | 250 |
Cardiac monitoring | |||||||||
ProBNP [ng/l] (<84) | 555 | - | 603 | - | - | - | - | - | 72 |
LVOT-gradient [mm Hg] | 20 | 18 | 20 | 20 | 13 | 8 | 9 | 7 | 5 |
PWT [cm] | 0.8 | 0.8 | 0.8 | 0.8 | 0.7 | 0.7 | 0.7 | 0.8 | 0.7 |
VST [cm] | 1.4 | 1.3 | 1.4 | 1.4 | 1.1 | 1.2 | 1.0 | 1.0 | 0.8 |