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Table 8 Diet treatment according to age group

From: Urea cycle disorders in Spain: an observational, cross-sectional and multicentric study of 104 cases

Age (N = 93) 0-1y (N = 4) 1-10y (N = 47) 11-18y (N = 20) >18y (N = 22)
Total proteins (g/kg/day) 1.86 (0.90-2.95) 0.95 (0.7-1.2) 0.84 (0.65-0.94) 0.7 (0.57-0.92)
Energy (calories) (kcal/kg/day) 102 (92.5-140) 72 (58-95) 40 (32-43,5) 36 (30-42)
Essential Aminoacids (g/kg/day) 0.39 (0.2-0.5) 0.3 (0.27-0.43) 0.25 (0.14-0.48) 0.2 (0.11-0.41)
Age <6 m 6-12 m 1-10y 11-16y >16y
WHO/FAO/UNU* (safe levels proteins) 1.77 1.31 0.92-1.14 0.84-0.90 0.84-0.87
UK practice (N = 45)** Proteins 2 (0.7-2.5) 1.6 (1.2-1.8) 1.3 (1-1.7) 0.9 (0.7-1.4) 0.8 (0.4-1.2)
  1. Data reflects median and IQR.
  2. N = number of patients on diet.
  3. y: years; m: months;* Who/FAO/UNU Expert consultation (2007) [32].
  4. **Adam et al. J Hum Nutr Diet 2013; 25: 398-404 [33].