Table 3 Summary of point prevalence data
MPS IV type | Point Prevalence | per 10,000 | Evidence of consanguinity | Evidence of ethnicity founder effect | Representative of whole country** | Point in time | Recommended Enzymatic analysis ǂ | Quality | |
|---|---|---|---|---|---|---|---|---|---|
Australia KOL [27] | MPS IVA | 1 in 926,000* | 0.0108* | NR | NR | Y | 30th June 2013 | Y | ungraded |
Denmark [33] | MPS IV (unclassified) | 1 per 323, 000* | 0.031* | NR | Y | Y | 31st Dec 2007 | Y | low |
Malaysia KOL [28] | MPS IVA | 1 per 1,872,000 | 0.005* | NR | NR | Y | 30th June 2013 | Y | ungraded |
UK KOL [29] | MPS IVA | 1 per 599,000* | 0.0167* | NR | Y | Y | Mid-2010 | Y | ungraded |