| Sporadic-LAM | TSC-LAM | ||
---|---|---|---|---|
Angiomyolipoma | Â | |||
Present | Absent | p value | ||
Number of patients | 53 | 54 | Â | 15 |
Mean age at respiratory presentation * (years) | 32.3 | 37 | 0.18 | 31.8 |
Mean disease duration * (years) | 14.4 | 15.2 | 0.21 | 10.5 |
Ever had pneumothorax # (%) | 16 (32) | 13 (24) | 0.37 | 40 |
Lymphatic disease detected # (%) | 6 (11) | 10 (19) | 0.036 | 13 |
Ever been pregnant # (%) | 29 (55) | 24 (44) | 0.07 | 33 |
Mean baseline FEV 1 * (% predicted) | 65.7 | 71.4 | 0.37 | 64 |
Mean baseline TL CO * (% predicted) | 57.7 | 59.3 | 0.79 | 47 |