From: Proposed guidelines for the diagnosis and management of methylmalonic and propionic acidemia
Age | Protein per 100 ml | Glucose polymer concentration | ±fat emulsion* | Energy | Energy | Suggested daily intake | Feeding frequency |
---|---|---|---|---|---|---|---|
% carbohydrate | % fat | kcal per 100 ml from CHO + fat | kJ per 100 ml | ml//kg | |||
Up to 12 m | Stop or reduce total protein intake by ≥50% depending on illness severity | 10 | 3.5 | 72 | 302 | 120 -150 ml/kg | Continuous tube feds using enteral feeding pump |
1-2 y | 15 | 5 | 105 | 441 | 1200 ml | ||
2-9 y | 20 | 5 | 125 | 525 | Estimated as indicated | ||
>10 y | 25 | 5 | 145 | 609 | Estimated as indicated |