| ≤ 6 months of age | > 6 months of age | Patients diagnosed via NBS |
---|---|---|---|
PTT | 80.5 seconds (SD: +/−40.6; median: 66.7; range: 39–181) | 49.8 seconds (SD: +/−16.1; median: 51; range: 13.3-89.4) | 84.4 seconds (SD: +/−39.1; median: 77.2; range: 45–168) |
AST | 113.3 U/l (SD: +/−116.7; median: 84.5; range: 29–613) | 98.1 U/l (SD: +/−41.7; median: 88.5; range: 30–201) | 45.5 U/l (SD: +/−21.9; median: 46; range: 18–72) |
ALT | 64.5 U/l (SD: +/−40.6; median: 59; range: 10–155) | 59.6 U/l (SD: +/−30.2; median: 57.5; range: 16–124) | 20.2 U/l (SD: +/−10.1; median: 21; range: 4–35) |
GGT | 158.2 U/l (SD: +/− 194.2; median: 97; range: (5–104) | 158.2 U/l (SD: +/−108.7; median: 124; range: 29–515) | 65.3 U/l (SD: +/−28.4; median: 66; range: 22–102) |