PKD
|
873
|
7
|
866
|
1106
|
13
|
1093
|
MCGN-II
|
27
|
0
|
27
|
28
|
0
|
28
|
Familial GN (Alport & Secondary FSGS)
|
106
|
12
|
94
|
130
|
4
|
126
|
Cystinosis
|
9
|
7
|
2
|
3
|
2
|
1
|
Oxalosis & Fabry Disease
|
12
|
0
|
12
|
9
|
0
|
9
|
MCKD
|
80
|
17
|
63
|
73
|
8
|
65
|
HUS
|
52
|
6
|
46
|
59
|
12
|
47
|
CAKUT
|
637
|
111
|
526
|
674
|
107
|
567
|
TSC
|
3
|
0
|
3
|
1
|
0
|
1
|
Alagille Syndrome
|
0
|
0
|
0
|
1
|
0
|
1
|
NPS
|
1
|
0
|
1
|
1
|
0
|
1
|
SRNS
|
12
|
0
|
12
|
7
|
0
|
7
|
BHD & VHL
|
5
|
0
|
5
|
1
|
0
|
1
|
Fanconi RTA
|
11
|
0
|
11
|
8
|
0
|
8
|
TOTAL GRD
|
1828
|
160
|
1668
|
2101
|
146
|
1955
|
TOTAL Non-GRD
|
9860
|
357
|
9503
|
17584
|
308
|
17276
|
% of Cohort GRD
|
18.52%
|
44.82%
|
17.53%
|
11.94%
|
47.40%
|
11.31%
|
Adult GRD CKD vs GRD Incident RRT
|
9.8% vs 17.53%, x2 < 0.0005, Relative risk 0.582, 95% CI 0.520-0.651
|
9.8% vs 11.31%, x2 0.014, Relative risk 0.869, 95% CI 0.790-956
|
Paediatric vs Adults GRD Incident RRT
|
44.81% vs 17.53%, x2 < 0.0005, Relative risk 3.574, 95% CI 2.919-4.375
|
47.4% vs 17.53%, x2 < 0.0005, Relative risk 6.645, 95% CI 5.338-8.272
|