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Table 1 Description of the case population studied

From: Adrenal hormonal imbalance in acute intermittent porphyria patients: results of a case control study

 

Gender

Age

Fertile

Heme arginate

PBG

ALA

GFR

F1

F

54

No

No

3

1

>60

F2

F

32

Yes

No

7

6

>60

F3

F

36

Yes

No

10

6

>60

F4

F

37

Yes

No

16

10

>60

F5

F

25

Yes

No

16

13

>60

F6

F

31

Yes

No

17

15

>60

M1

M

52

Yes

No

19

9

>60

F7

F

49

Yes

No

23

11

>60

F8

F

34

Yes

No

26

21

>60

F9

F

35

Yes

No

28

12

>60

F10

F

31

Yes

No

29

7

>60

F11

F

35

Yes

No

30

23

>60

F12

F

34

Yes

No

30

12

>60

F13

F

27

Yes

No

32

22

>60

F14

F

42

Yes

No

32

21

52.84

F15

F

51

No

No

34

31

>60

F16

F

22

Yes

No

34

15

>60

F17

F

29

Yes

No

35

16

>60

F18

F

41

Yes

No

37

27

>60

F19

F

31

Yes

No

45

20

>60

F20

F

20

Yes

No

52

42

>60

M2

M

53

Yes

Yes

57

41

> 60

F21

F

31

Yes

Yes

63

40

>60

F22

F

41

Yes

Yes

64

40

>60

  1. Heme arginate treatment: Normosang®; 3 mg/Kg; every 2–3 weeks; PBG: porphobilinogen concentrations (nmol/mmol creatinine); ALA: aminolevulinic acid concentrations nmol/mmol creatinine). GFR: glomerular filtration rate (mls/min).