|
Patients (N)
|
27 (21 males)
|
15 (9 males)
| |
|
Median age at diagnosis (months)
|
75 (range 39–192)
|
42 (range 12–101)
|
<0.001*
|
|
Median ALT at diagnosis (UI/L)
|
251 (range 23–582)
|
110 (range 12–502)
|
0.022*
|
|
Median AST at diagnosis (UI/L)
|
114 (range 27–205)
|
67 (range 22–168)
|
0.059 (NS)
|
|
Median GGT at diagnosis (UI/L)
|
72 (range 11–267)
|
21 (range 13–119)
|
0.019*
|
|
Basal urinary copper (μg/24 h)
|
150 (range 14–413)
|
31 (range 4–780)
|
0.91 (NS)
|
|
Median liver copper content (μg/g dry tissue)
|
780 (range 60–1660)
|
989 (range 407–1230)
|
0.423 (NS)
|
