First symptoms | Late-infantile (n = 23) | Juvenile (n = 36) | p | ||
---|---|---|---|---|---|
n | % | n | % | ||
Gait disturbance | 16 | 70% | 25 | 69% | 0.9922 |
Pain | 6 | 26% | 5 | 14% | 0.2447 |
Abnormal movement patterns | 14 | 61% | 25 | 69% | 0.5011 |
Impaired fine motor skills | 4 | 17% | 22 | 61% | 0.0011 |
Restlessness/irritability | 4 | 17% | 10 | 28% | 0.3645 |
Weakness | 10 | 43% | 13 | 36% | 0.5748 |
Problems in concentration | 0 | 0% | 23 | 64% | 0.0001 |
Behavioural problems | 3 | 13% | 20 | 56% | 0.0012 |
Developmental regression in general | 14 | 61% | 19 | 53% | 0.5449 |