Age in years (median  IQR)

17.7 (9.5–28.1)

15.8 (9.7–26.7)

19.6 (10.9–31.9)

14.2 (6.7 – 24.5)

0.14

Years since diagnosis (median – IQR)

4.3 (0.0–11.4)

4.3 (0.4–9.0)

3.6 (0.0–12.8)

5.3 (0.0–11.5)

0.88

Weight zscore (mean  SD)

−0.12 (1.25)

−0.25 (1.25)

0.07 (1.33)

−0.51 (0.97)*

0.16

Height zscore (mean  SD)

−0.63 (1.23)*

−0.53 (1.14)*

−0.64 (1.26)*

−0.91 (1.32)*

0.67

BMI zscore (mean  SD)

0.15 (1.23)

0.02 (1.17)

0.41 (1.22)

−0.25 (1.31)

0.10

Chronic cough, n (%)

136 (81.0)

48 (81.4)

65 (87.8)

23 (65.7)

0.13

Chronic sputum production, n (%)

113 (81.9)

43 (81.1)

52 (83.9)

18 (78.3)

0.83

Clubbing, n (%)

31 (18.5)

10 (16.9)

16 (21.6)

5 (14.3)

0.57

Nasal secretions, n (%)

136 (81)

49 (83.1)

60 (81.1)

27 (77.1)

0.63

FEV_{1} zscore (median  IQR) (n = 112)

−1.79 (−2.96; –0.76)*

−1.47 (−2.67; –0.47)*

−1.94 (−3.13; –1.19)*

−2.34 (−3.61; –0.55)*

0.17

FVC zscore (median  IQR) (n = 112)

−0.76 (−1.61; –0.15)*

−0.54 (−1.43; 0.06)*

−0.98 (−1.77; –0.21)*

−0.77 (−2.05; –0.30)*

0.75
