Table 3 Age at onset, progression, and severity of sensorineural deafness before CI in 10 MYH9 -RD patients
From: Cochlear implantation is safe and effective in patients with MYH9-related disease
Patient/ family | Age at onset1 | Age at first use of hearing aids | Age at evolution toward PTA > 70 dB NHL | Age at CI | PTA before CI right/left2 |
|---|---|---|---|---|---|
1/1 | 20 | 23 | 24 | 34 | 87/82 |
2/2 | 20 | 30 | 32 | 40 | 115/120 |
3/3 | 8 | 34 | 34 | 43 | 91/110 |
4/4 | 17 | 64 | 70 | 72 | 107/106 |
5/5 | 20 | 25 | 25 | 27 | 78/91 |
6/6 | 25 | 48 | 48 | 50 | 118/116 |
7/7 | 3 | 5 | 8 | 12 | 97/104 |
8/7 | 4 | 13 | 19 | 30 | 121/111 |
9/7 | 19 | 21 | 24 | 46 | 126/121 |
10/8 | 30 | 33 | 44 | 54 | 100/85 |
Mean (SD) | 16.6 (9) | 29.6 (17) | 32.8 (17) | 40.8 (16) | Â |